Cystic Fibrosis Life Expectancy
Cystic fibrosis is a genetic disorder that damages many of the body's organs and shortens life expectancy. Often people with cystic fibrosis and family members need help to adjust psychologically and emotionally. They also need help to manage the demands of treatment. We looked for trials of psychological treatments in people with cystic fibrosis and their families. The review includes 13 studies with 529 people of mainly behavioural and educational treatments. Some treatments aimed to improve people's ability to cope with the disease or genetic risk. Other treatments aimed to improve dietary intake and boost the effectiveness of chest physiotherapy. Some evidence showed that behavioural treatments can improve emotional outcomes for people with cystic fibrosis and their carers. We also found some evidence that psychoeducational treatments can improve knowledge in the short term. In addition, educational and behavioural treatments can help nutrition and growth in people with cystic fibrosis. However, at the moment there is no clear evidence to show the best psychological treatments to help people with cystic fibrosis and their carers. There should be multicentre trials to improve adherence to treatment.